What is lobe sequestration?
Pulmonary sequestration is a condition in which a segment or lobe of dysplastic lung tissue exists with no communication with the rest of the tracheobronchial tree and receives an anomalous systemic vascular supply, separate from the rest of the lung.
How is pulmonary sequestration diagnosed?
Diagnosis. Pulmonary sequestrations are diagnosed with a prenatal ultrasound showing a mass in the chest of the fetus. The mass may displace the heart from its normal position or push the diaphragm downward, but the key feature of a sequestration is the artery leading from the cystic mass directly to the aorta.
What causes pulmonary sequestration?
Pulmonary sequestration is a rare congenital (present from birth) malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation.
What is Extralobar pulmonary sequestration?
Bronchopulmonary sequestration, also known as BPS or pulmonary sequestration, is a rare birth defect in which an abnormal mass of nonfunctioning lung tissue forms during prenatal development. It can form outside (extralobar) or inside (intralobar) the lungs, but is not connected directly to the airways.
Is pulmonary sequestration serious?
While it is not in itself a life-threatening condition, a pulmonary sequestration can cause health complications including cardiovascular problems, long-term infections like tuberculosis, and bronchial cancer. It could be fatal if blood vessels in the lung begin to hemorrhage.
What is the most common type of pulmonary sequestration?
An intralobar sequestration is the most common form of the disease where the lung malformation remains within the visceral pleura of its lobe, whereas the extralobar type corresponds to a true accessory lung, with a separate pleural envelope and an aberrant venous drainage [7].
What is the most common form of pulmonary sequestration?
What is considered the gold standard for diagnosis of pulmonary sequestration?
However, the gold standard for identifying the pulmonary sequestration recently is CT/MR angiography as it confirms the anatomy, identifies the anomalous systemic arterial supply, and shows the venous drainage [5].